Blount's Disease

 

BlountsBlounts eight platesBlounts osteotomy

 

Types

 

Infantile Adolescent

Onset 1 - 3 years

Bilateral

Most common

Onset > 6 years

Unilateral

Rare

 

Definition

 

Infantile tibia vara

- progressive varus deformity of knees

- secondary to abnormality of medial upper tibial physis

 

Epidemiology

 

African descent / females / obesity / bilateral

 

Etiology

 

Disruption of normal medial endochondral bone formation

 

Unknown / multifactorial

- genetic and racial predisposition

- abnormal compression on medial side of proximal tibial physis

- obesity

 

Clinical

 

Bilateral & symmetrical bowing

- age 1 - 3

- walking

- normal physiological varus should resolve by age 2

 

Varus knee

Internal tibial torsion - due to the tethering affect of the fibula

 

X-ray

 

BlountsBlounts

 

Findings

- medial beaking of the epiphysis

- widened and irregular medial physis

- medial sloping of the epiphysis

- metaphyseal varus

 

Severe knee varus / lateral thrust / lateral collateral ligament insufficiency

 

Distal femoral varus also common

 

BlountsBlountsBlounts

 

Metaphyseal-Diaphyseal Angle Medial physeal slope

Line perpendicular to axis of tibia

Line through medial and lateral metaphyseal beaks

 

Line through medial physis

Line through lateral physis

Physiologic bow legs < 11°

Blount's > 11°

Definitive Blount's > 16o

High risk of progression if > 60°
MDA Metaphyseal angle

 

CT

 

Used to identify presence of physeal bar

 

Langenskiold Classification

 

Six stages

- stages I - III: reversible with bracing

- stages IV - VI: permanent damage to eiphysis / need surgery

 

Stage I Stage II Stage III
Medial beak Medial saucer shaped defect Develop step
Age 2 - 3 Age 2 - 4 Age 4 - 6

 

BlountsBlountsBlounts

 

Stage IV Stage V Stage VI

Narrow physis

Step deepens

Medial epiphysis splits into two

Physeal bar

Medial growth arrest

Develop severe varus

Age 5 - 10 Age 9 - 11 Age 10 - 13

 

BlountsBlountsBlounts

 

Differential diagnosis

 

Ricketsachondroplasia

Rickets                                                              Achondroplasia

 

Physiological varus - normal growth plate, metaphyseal-diaphyseal angle < 11°

Ricket's / renal osteodystrophy - widened physes / cupped metaphyses / flared distal distal

Skeletal dysplasia - metaphyseal chondrodysplasia, achondroplasia

Trauma / tumour / infection

Osteogenesis imperfecta

Juvenile rheumatoid arthritis

 

Natural history

 

Progresses to severe osteoarthritis by early adulthood

 

Disease progression 

- metaphyseal-diaphyseal angle >16°  - 95% chance of progression

- metaphyseal-diaphyseal angle < 11° - 95% chance of spontaneous resolution

- metaphyseal-diaphyseal angle < 11 - 16° - close observation

 

Management 

 

Brace / KAFO

 

AFO Blounts

Montenegro NB, Massa BSF, De Angeli LRA. Available from URL: http://www.scielo.br/aob.

 

Indications

 

< 3 with unilateral disease

Langeskiold stage I & II

Able to wear brace  / obesity

Wear at night time

 

Results

 

Up to 50% failure

Poor compliance

 

Surgical options

 

Guided growth / temporary hemiepiphysiodesis

Osteotomy and acute correction 

Osteotomy and gradual correction with frame 

Medial tibial plateau elevation

Combined

 

Results

 

Ramella et al J Clin Med 2023

- systematic review of surgical treatment of 1600 knees with Blount's

- acute correction 47%, hemiepiphysiodesis 22%, gradual correction 18%, combined 13%

- overall recurrence 18%

- recurrence: gradual correction 7%, hemiepiphysiodesis 29%

- increasing recurrence rate with increasing age

 

Guided growth / temporary hemiepiphysiodesis

 

Blounts guided growthBlounts Guided growth

 

Indication

 

Lagenskiold stage I & II

Mild to moderate deformity

No physeal bar in medial growth plate

 

Technique

 

Blounts Eight platesBlounts eight plates

 

Eight platesEight plates

 

Eight plate surgical technique PDF

 

Arthroscopy techniques guided growth PDF

 

Results

 

Jain et al J Pediatr Orthop 2020

- 61 limbs with Blount's treated with tension band plates

- 41% overall surgical failure rate: more common with severe deformity

- 11% mechanical failure - more common with titanium and cannulated screws

 

BlountsBlountsBlounts

 

Osteotomy with acute correction

 

Indication

 

Langenskiold Stage III - VI

Medial physeal bar

Moderate deformity

 

Types 

 

Opening / closing wedge

Dome

Oblique osteotomy - Rab biplanar oblique osteotomy

 

Blounts osteotomyBlounts osteotomyBlounts osteotomy

 

Technique

 

Rab osteotomyRab osteotomy

Rab oblique osteotomy

 

Blounts osteotomyBlounts osteotomyBlounts osteotomyBlounts osteotomy

Rab oblique osteotomy

 

Surgical technique oblique osteotomy PDF

 

Osteotomy performed distal to tibial tuberosity

- must osteotomise fibula

- must release anterior compartment to prevent compartment syndrome

- also correct deformity internal tibial torsion at same time

- fixation with K wires / screws / plates

- cast postoperatively

- +/- temporary hemiepiphysiodesis lateral

- +/- medial physeal bar resection

- +/- medial tibial plateau elevation

 

Results

 

Mare et al J Pediatr Orthop 2021

- 20 patients mean age of 4 treated with acute proximal dome osteotomy

- 40% recurrence at 4 year follow up

- increased risk with increased Langenskiold stage / severe deformity / increased medial physeal slope

 

Osteotomy with gradual correction using external fixation

 

Blounts frameBlounts frameBlounts frame

 

Technique

 

Vumedi Taylor Spatial Frame for severe Blount's deformity video

 

Vumedi principles of frame correction for Blount's disease video

 

POSNA Taylor Spatial Frame Correction for severe Blount's video

 

Results

 

Mare et al Strategies Trauma Limb Recon 2022

- 25 severe or recurrent Blount's treated with hexapod external fixation

- alignment after correction: 55% good, 35% acceptable, 10% poor 

- mean time in external fixator 136 days

- 100% incidence pin site infections

 

Lateral epiphysiodesis + medial metaphyseal elevation osteotomy

 

Blounts Elevation

 

Indications

 

Langenskiold Stages V & VI 

Medial physeal bar

 

Technique

 

Lateral epiphysiodesis

Fibular osteotomy

Lateral compartment release

Medial elevation osteotomy

+/- epiphysiodesis of contralateral knee to prevent leg length discrepancy

 

Results

 

Hussein et al J Orthop Surg Res 2025

- 24 patients with Langenskiold Stage V and VI 

- medial plateau elevation and external fixator

- mean time in frame 14 weeks

- recurrence in 21%