Background
Definition Short Stature
< 1.25 m in adult
Types
1. Proportionate dysplasia
- mucopolysaccharidoses
- Morquio's, Hurler's, Hunter's
2. Dysproportionate dysplasia
- short trunk / SED
- short limb / achondroplasia & MED
Proportionate dysplasia / Symmetrical decrease in limb and trunk length