containment

Multiple epiphyseal dysplasia

Definition 

 

Disturbance of endochrondral ossification of epiphyses of tubular bones

- preservation of vertebrae (c.f. SED)

 

Characteristics

 

Dysproportionate dwarfism with normal trunk

- not as severe as achondroplasia

- usually 145 - 170 cm tall

 

Characterised by small flattened irregular epiphyses

- symmetrical

- leads to OA by 3-4th decade

 

Management

Aim

 

Prevent head deformity & secondary OA

- interfere as little as possible with child's development

 

Goals

 

1. Restore & maintain ROM

- allow abduction which covers anterolateral extruded head 

- important range is abduction in extension

- aim 30o abduction or 75% of contralateral side 

- can consider adductor tenotomy