Arthrogryposis Multiplex Congenita
Definition
AMC characterised by non progressive congenital rigidity of 2 or more joints
- Arthrogryposis means curved joint
- Arthrogryposis refers to 150 syndromes
Types
1. Amyoplasia
- involves all 4 limbs
2. Distal Arthrogryposis
- AD
- type 1 98% hand / 87% feet