cervical

Spondyloepiphyseal dysplasia

Type

 

Disproportionate dwarfism with a short trunk

 

Problems with dwarfism, spine, vision and hearing

 

Definition

 

Primary involvement of vertebrae & epiphyseal centres of limbs

 

Resulting short-trunk dwarfism

- Limb are short, but trunk is even shorter

 

(cf Metaphyseal Chondrodysplasia - Short limbed Dwarf)

 

Types

 

DISH

Definition

 

Diffuse Idiopathic Skeletal Hyperostosis

- non-inflammatory disease

- ossifying enthesopathy / bone forming diasthesis

- most commonly involves spine / anterior longitudinal ligament

 

AKA  Forestier's disease

 

DDx

 

Ankylosing Spondylosis

 

DISH

- non inflammatory

- no facet or SIJ involvement

- no squaring of anterior vertebral body